Korean J Gastroenterol.
2000 Aug;36(2):250-254.
A Case of Angiomyolipoma of the Ileum
Abstract
- Angiomyolipoma is a mesenchymal hamartoma composed of blood vessels, smooth muscle, adipose tissue, and supporting connective tissue. It is occasionally associated with tuberous sclerosis. Most of angiomyolipoma arises in the kidney and gastrointestinal angiomyolipoma is very rare. We experienced a case of symptomatic ileal angiomyolipoma, which was the first documented case. A 60-year-old female was admitted to our hospital because of intermittent periumbilical pain. In the physical examination, slightly painful abdominal mass was palpated. Abdominal ultrasonography and computed tomography suggested intussusception. The patient underwent a segmental resectioin of the ileum. Postoperative gross finding showed 4x4x3 cm mass having yellowish resection plane without hemorrhage and necrosis in the terminal ielum. Microscopic fingings of the mass revealed intermixed adipose tissue, blood vessels, and smooth muscle bundles. Immunohistochemically, the proliferating smooth muscle cells were positive for vimentin. Pathologic findings confirmed the diagnosis of angiomyolipoma of ileum.
