Ann Dermatol.  2009 May;21(2):217-220. 10.5021/ad.2009.21.2.217.

A Case of a Cutaneous Angiomyolipoma

• Shin JU
• Lee KY
• Roh MR

• KMID: 2219402
• DOI: http://doi.org/10.5021/ad.2009.21.2.217

Abstract

A cutaneous angiomyolipoma, which is also known as a cutaneous angiolipoleiomyoma, is a rare benign mesenchymal tumor. Only 18 cases have been reported in the English literature. We describe a case of an angiomyolipoma presenting on the right ear helix of a 26-year-old female. The histopathologic examination revealed a typical form of an angiomyolipoma with a proliferation of mature adipocytes. As with all previously reported cases, our patient did not present with the stigmata of tuberous sclerosis. This is the 20th reported case of cutaneous angiomyolipoma and the 3rd reported case in Korea.

Keyword

Angiolipoleiomyoma; Angiomyolipoma

MeSH Terms

Adipocytes
Adult
Angiomyolipoma
Christianity
Ear
Female
Humans
Tuberous Sclerosis

Figure

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  Fig. 1 Pea-sized blue nodule on the helix of the left ear.

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  Fig. 2 Hematoxylin-eosin-stained section shows variable-sized blood vessels, smooth muscle bundles, and mature adipose tissue (A: ×40, B: ×100).

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  Fig. 3 Masson trichrome stained the muscular portions of the tumors bright red and the collagen blue (×100).

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  Fig. 4 Elastica van Gieson staining stained small arterioles within the lesions (×100).

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