Korean J Urol.
2003 Apr;44(4):386-389.
Malignant Rhabdoid Tumor of Kidney in Infant
- Affiliations
-
- 1Department of Urology, Dae Dong Hospital, Korea.
- 2Department of Urology, College of Medicine, Pusan National University, Busan, Korea. lsd@hyowon.pusan.ac.kr
- 3Department of Pediatrics, College of Medicine, Pusan National University, Busan, Korea.
- 4Department of Urology, Pathology, College of Medicine, Pusan National University, Busan, Korea.
Abstract
- A malignant rhabdoid tumor of the kidney, an uncommon renal tumor of children, is one of the most lethal neoplasms in early life. It was considered to be a sarcomatous variant of Wilms' tumor; however, further studies of its histological and clinical characteristics have proven it to be a distinct entity. We report a case of malignant rhabdoid tumor of the kidney in a 3-month-old girl, with a left abdominal palpable mass that had developed over the previous month. A left radical nephrectomy, with a regional lymph node biopsy, and 4 cycles of adjuvant chemotherapy, was performed. On the 45th postoperative day, multiple metastasises in liver, contralateral kidney and left upper lobe of lung were found. The patient expired 2 months after the operation.
