J Korean Pediatr Soc.
1999 Sep;42(9):1292-1297.
A Case of Malignant Extrarenal Rhabdoid Tumor
- Affiliations
-
- 1Department of Pediatrics, Wonju College of Medicine, Yonsei University, Wonju, Korea.
- 2Department of Orthopedic Surgery, Wonju College of Medicine, Yonsei University, Wonju, Korea.
- 3Department of Pathology, Wonju College of Medicine, Yonsei University, Wonju, Korea.
- 4Department of Radiology, Wonju College of Medicine, Yonsei University, Wonju, Korea.
Abstract
- Malignant Rhabdoid tumor is a rare malignant neoplasm and is morphologically similar to rhabdomyosarcoma, but is different immunohistochemically. Most malignant rhabdoid tumors occur in the kidney of infants, and are rarely reported at extrarenal sites. Since Frierson and his collagues first described the malignant extrarenal rhabdoid tumor(MRT) in children in 1985, it has rarely been reported. The neoplasm is histologically and immunohistochemically identical to a renal malignant rhabdoid tumor. There have been no previous reports of this neoplasm in Korea. An MRT of the sacroiliac bone in a 11-year-old girl is described. Five months after the initial presentation, the patient is still alive with partial response to combination chemotherapy and radiotherapy. The authors review previous reports of extrarenal MRT, and discuss the pathologic characteristics, differential diagnosis, and treatment of this rare neoplasm.
Keyword
- Full Text Links
-
- Actions
-
Cited
- CITED
-
- Close
- Share
-
- Similar articles
-
- A Case of Malignant Extrarenal Rhabdoid Tumor of the Retroperitoneum
- Imaging Findings of a Malignant Rhabdoid Tumor in the Stomach: A Case Report
- A Case of Malignant Rhabdoid Tumor on the Face
- Malignant Extrarenal Rhabdoid Tumor of the Pelvic Paravertebral Region: Case Report
- A Case of Malignant Rhabdoid Tumor in the Anterior Mediastinum
