Korean J Pediatr Hematol Oncol.  2001 Oct;8(2):372-377.

A Case of Malignant Extrarenal Rhabdoid Tumor of the Retroperitoneum

• Kim SA
• Hong JH
• Lyu CJ
• Yang CH
• Kim KY

Abstract

Malignant rhabdoid tumor is a clinically aggressive neoplasm that was initially described as a distinctive renal tumor of childhood. But among the malignant rhabdoid tumors, extrarenal rhabdoid tumor is rare. We report an extrarenal neoplasm histologically and ultrastructurally identical to renal rhabdoid tumor that arose in the retroperitoneum of a 4-month-old boy and presented as a right lower abdominal mass. The tumor had an aggressive clinical course despite multimodal therapeutic regimens, and the patient died with disseminated disease 12 months after diagnosis.

Keyword

Rhabdoid tumor; Extrarenal

MeSH Terms

Diagnosis
Humans
Infant
Male
Rhabdoid Tumor*