Korean J Pediatr.  2008 Sep;51(9):1018-1022. 10.3345/kjp.2008.51.9.1018.

A case of testicular adrenal rest tumor in a male child with congenital adrenal hyperplasia

• Kim JH
• Yun KA
• Shin CH
• Yang SW

• KMID: 2280199
• DOI: http://doi.org/10.3345/kjp.2008.51.9.1018

Abstract

Testicular adrenal rest tumors are a well-known complication in male patients with congenital adrenal hyperplasia. Corticosteroid suppressive therapy usually results in the regression of these tumors. We describe a patient with 21-hydroxylase deficiency who developed bilateral testicular masses. Despite steroid suppressive therapy, the tumors did not regress and hormonal control was poor. Consequently, bilateral partial orchiectomies were performed.

Keyword

Testicular neoplasms; Adrenal rest tumor; Child; Congenital adrenal hyperplasia; Steroid; 21-hydroxylase

MeSH Terms

Adrenal Hyperplasia, Congenital
Adrenal Rest Tumor
Child
Humans
Male
Orchiectomy
Steroid 21-Hydroxylase
Testicular Neoplasms
Steroid 21-Hydroxylase