Anesth Pain Med.  2010 Jul;5(3):260-263.

Anesthetic management of a patient with Kasabach-Merritt syndrome: A case report

• Park SC
• Yoon JY
• Hong JM
• Yoon JU
• Byeon GJ

Abstract

Kasabach-Merritt syndrome presents various problems for anesthetic management, which include thrombocytopenia, bleeding tendency, and problems arising from the hemangioma mass itself. A 1-month-old male was given sclerotherapies, platelet transfusions, steroid, interferon alpha, vincristine because of the bleeding from the right lower leg hemangioma, but platelet numbers were decreased and seizures occurred due to frontal lobe focal hemorrhage. After all, he was scheduled for his right lower leg amputation when he was 7 months old. Anesthesia was carefully induced with thiopental, rocuronium, fentanyl, and flexible bronchoscope. It was maintained with sevoflurane and air/oxygen with fentanyl injection. Although excessive bleeding was expected during anesthesia and surgery, the operation was performed without correction of platelet number. Two days later, postoperative course was improved almost normal.

Keyword

Anesthetic management; Kasabach-Merritt syndrome; Thrombocytopenia

MeSH Terms

Amputation
Androstanols
Anesthesia
Bronchoscopes
Fentanyl
Frontal Lobe
Hemangioma
Hemorrhage
Humans
Infant, Newborn
Interferon-alpha
Kasabach-Merritt Syndrome
Leg
Male
Methyl Ethers
Platelet Count
Platelet Transfusion
Sclerotherapy
Seizures
Thiopental
Thrombocytopenia
Vincristine
Androstanols
Fentanyl
Interferon-alpha
Methyl Ethers
Thiopental
Vincristine