J Korean Neurol Assoc.  2019 Feb;37(1):51-54. 10.17340/jkna.2019.1.8.

Posterior Reversible Encephalopathy Syndrome in a Patient with Systemic Lupus Erythematosus and Systemic Sclerosis Overlap Syndrome

• Song YM

• KMID: 2449292
• DOI: http://doi.org/10.17340/jkna.2019.1.8

Abstract

Posterior reversible encephalopathy syndrome (PRES) is characterized by neurotoxic symptoms and neuroimaging finding of reversible cerebral edema in association with various conditions including hypertension, eclampsia, and autoimmune diseases. The author experienced a 47-year-old woman with systemic lupus erythematosus and systemic sclerosis overlap syndrome who developed PRES. The patient presented with alteration of consciousness in association with hypertension and increased autoimmune activity. Magnetic resonance imaging revealed vasogenic edema in the bilateral cerebral cortex, subcortical white matter, basal ganglia, brainstem, and cerebellum.

Keyword

Posterior reversible encephalopathy; Systemic lupus erythematosus; Systemic sclerosis

MeSH Terms

Autoimmune Diseases
Basal Ganglia
Brain Edema
Brain Stem
Cerebellum
Cerebral Cortex
Consciousness
Eclampsia
Edema
Female
Humans
Hypertension
Lupus Erythematosus, Systemic*
Magnetic Resonance Imaging
Middle Aged
Neuroimaging
Posterior Leukoencephalopathy Syndrome*
Pregnancy
Scleroderma, Systemic*
White Matter