Res Vestib Sci.  2018 Mar;17(1):28-35. 10.21790/rvs.2018.17.1.28.

Autoimmune Inner Ear Disease Mimicking Bilateral Ménière's Disease: A Case Report

• Kim HJ
• Choi YG
• Kim HJ
• Kim KS

• KMID: 2408595
• DOI: http://doi.org/10.21790/rvs.2018.17.1.28

Abstract

Autoimmune inner ear disease (AIED) is a rare disease, accounting for < 1% of all cases of hearing impairment or dizziness. It is characterized by sensorineural hearing loss (SNHL) or vestibular dysfunction that results from an immunemediated process. Clinical features of AIED is SNHL that progresses over weeks to month with fluctuating hearing symptoms. Because there are no diagnostic laboratory and clinical feature, response to immunosuppressive therapy were important for diagnosis of AIED. Many diseases such as sudden SNHL and Meniere disease may also mimic AIED, a broad differential must be maintained in patients suspected of having AIED. We report a case of a 46-year-old female who presented with sudden hearing loss and vertigo. We could diagnose her as AIED with systemic lupus erythematous. The symptoms were improved treated with steroids.

Keyword

Autoimmune inner ear disease; Systemic lupus erythematous; Sensorineural hearing loss

MeSH Terms

Diagnosis
Dizziness
Ear, Inner*
Female
Hearing
Hearing Loss
Hearing Loss, Sensorineural
Hearing Loss, Sudden
Humans
Labyrinth Diseases*
Meniere Disease*
Middle Aged
Rare Diseases
Steroids
Vertigo
Steroids