Korean J Thorac Cardiovasc Surg.  2015 Feb;48(1):90-94. 10.5090/kjtcs.2015.48.1.90.

A Successfully Treated Case of Gorham-Stout Syndrome with Sternal Involvement

• Kim BJ
• Kim TH
• Kim DJ
• Noh D
• Haam SJ
• Lee S

• KMID: 2382236
• DOI: http://doi.org/10.5090/kjtcs.2015.48.1.90

Abstract

Gorham-Stout Syndrome (GSS) is a rare disease characterized by localized bone resorption. Any part of the skeleton may be affected; therefore, symptoms can vary depending on the site involved. Pathological analysis reveals lymphovascular proliferation and osteolysis in the affected lesion, but the etiology of the disease is poorly understood. When GSS occurs in the chest, chylothorax or respiratory failure may occur. Thus far, a standard treatment for GSS has not been established, and the prognosis remains unknown. The following case report describes a successfully treated case of GSS in a 16-year-old boy with an affected sternum and ribs.

Keyword

Sternum; Gorham-Stout Syndrome

MeSH Terms

Adolescent
Bone Resorption
Chylothorax
Humans
Male
Osteolysis
Prognosis
Rare Diseases
Respiratory Insufficiency
Ribs
Skeleton
Sternum
Thorax