J Korean Neurol Assoc.  2000 Jul;18(4):450-453.

A Case of Bilateral Anterior Opercular Syndrome: Foix-Chavany-Marie Syndrome

Affiliations
  • 1Department of Neurology, Seoul Municipal Boramae Hospital.
  • 2Department of Radiology, Seoul Municipal Boramae Hospital.
  • 3Department of Neurology, College of Medicine, Seoul National University.

Abstract

Bilateral opercular syndrome or Foix-Chavany-Marie syndrome (FCMS) is characterized by facio-pharyngo-glosso-masticatory diplegia with an automatic-voluntary movement dissociation, which is usually caused by bilateral fron-toparietal opercular lesions. A 52 year-old man suddenly developed left hemiplegia and also presented with anarthria, dysphagia, difficulty in jaw opening and mastication. However, involuntary swallowing and slight control of jaw move-ments were partly preserved. His gag reflex was decreased and emotional incontinence was absent. Brain magnetic res-onance (MR) imaging revealed high signal lesions in the right middle cerebral artery territory and left anterior opercu-lum. Severe stenosis of the right middle cerebral artery was observed on a MR angiogram. Rehabilitation training by cueing has improved his ability to open the mouth. To our knowledge, this is the first report of FCMS in Korea, and a cautious differential diagnosis of pseudobulbar palsy or buccofacial apraxia may be crucial.

Keyword

Bilateral anterior opercular syndrome; Foix-Chavany-Marie syndrome; Operculum; Automatic-voluntary dissociation

MeSH Terms

Apraxias
Brain
Constriction, Pathologic
Cues
Deglutition
Deglutition Disorders
Diagnosis, Differential
Hemiplegia
Humans
Jaw
Korea
Mastication
Middle Aged
Middle Cerebral Artery
Mouth
Pseudobulbar Palsy
Reflex
Rehabilitation
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