J Korean Ophthalmol Soc.
1989 Apr;30(2):305-309.
A Case of Anterior Lenticonus in Alport's Syndrome
- Affiliations
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- 1Department of Ophthalmology, School of Medicine, Soon Chun Hyang University, Seoul, Korea.
Abstract
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Alport's syndrome, first described by Alport in 1927, is a clinical entity which consists of lens abnormalities, hereditary hemorrhagic nephritis and nerve deafness. Anterior lenticonus is a rare structual anomaly of lens in which there is a conicalor spherical protrusion of the anterior lens surface into the anterior chamber as a characteristic finding of Alport's syndrome. The authers experienced a case of Alport's syndrome in a 22-year-old man associated with bilateral anterior and posterior lenticonus, hematuria, proteinuria, renal failur earld nerve deafness(complete form).