Tuberc Respir Dis.  2001 Feb;50(2):245-251. 10.4046/trd.2001.50.2.245.

A Case of Lymphangioleiomyomatosis with Renal Angiomyolipoma

• Kang SB
• Park SJ
• Lee SH
• Jung DY
• Yoo JH
• Kim JY
• Park IW
• Choi BW
• Son DS
• Kim MK

• KMID: 2318305
• DOI: http://doi.org/10.4046/trd.2001.50.2.245

Abstract

Recently we have experienced one case of pulmonary lymphangioleiomymatosis(LAM). A 49 year-old woman visited the outpatient department complaining of longstanding dyspnea, which was aggravated by exercise. Although the chest PA film showed nothing more than a slight increase in interstitial marking, a lung HRCT revealed multiple cystic lesions of a similar size that were scattered through out the whole field in both lungs. An abdominal CT detected an angiomyolipoma located in the midbody of the left kidney. Video-assisted thoracic surgery(VATS) was performed for the pathologic diagnosis. On gross examination of the biopsy lung, a pulmonary LAM was confirmed by a finding of smooth muscle proliferation in the interstitum of the lung. After the final diagnosis, oral medroxyprogesterone was prescribed and she is presently in a stable condition.

Keyword

Pulmonary lymphangioleiomyomatosis; Renal angiomyolipoma; VATS; Medroxyprogesterone

MeSH Terms

Angiomyolipoma*
Biopsy
Diagnosis
Diagnosis, Oral
Dyspnea
Female
Humans
Kidney
Lung
Lymphangioleiomyomatosis*
Medroxyprogesterone
Muscle, Smooth
Outpatients
Thoracic Surgery, Video-Assisted
Thorax
Tomography, X-Ray Computed
Medroxyprogesterone