J Dent Anesth Pain Med.  2015 Dec;15(4):251-255.

An 18-year-old patient with Prader-Willi syndrome: a case report on dental management under sedation and general anesthesia

• Song KU
• Nam OH
• Kim MS
• Choi SC
• Lee HS

Abstract

Prader-Willi syndrome (PWS) is a rare genetic disorder reported rarely in dentistry. Dental practitioners should know the features of PWS because affected patients have a variety of dental symptoms. The current report describes a case of PWS. An 18-year-old male patient presented with traumatic injuries. Initial emergency treatments were performed under sedation, and further treatments were conducted under general anesthesia. After adequate healing, periodic follow-up and dietary management according to the patient's age and nutritional phase were recommended. Dental management of PWS patients consists of active preventive measures in addition to dietary consultation according to age and nutritional phase.

Keyword

Conscious sedation; Dental practice management; General anesthesia; Hyperphagia; Prader-Willi syndrome

MeSH Terms

Adolescent*
Anesthesia, General*
Conscious Sedation
Dentistry
Emergency Treatment
Follow-Up Studies
Humans
Hyperphagia
Male
Practice Management, Dental
Prader-Willi Syndrome*

Figure

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  Fig. 1 (A) Characteristic facial features including narrow forehead, thin upper vermillion, and downturned corners of the mouth were observed. The patient also had a typical body habitus, with narrow shoulders and obesity, (B) Preoperative clinical examination revealed crown fracture of the maxillary central incisors with pulp involvement, (C) The postoperative photograph shows prosthodontic treatment of the right and left maxillary central incisors.

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  Fig. 2 Because of poor cooperation, the preoperative panoramic radiograph was blurred.

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