Korean J Anesthesiol.  2004 Sep;47(3):439-441. 10.4097/kjae.2004.47.3.439.

Anesthetic Management in Pediatric Patient with Prader-Willi Syndrome: A case report

• Min SH
• Lim CH
• Lee HW
• Lim HJ
• Yoon SM
• Chang SH

• KMID: 2299118
• DOI: http://doi.org/10.4097/kjae.2004.47.3.439

Abstract

Prader-Willi syndrome is brought by chromosomal abnormality and is characterized by mental retardation, morbid obesity, infantile hypotonia, hypogenitalism. While feeding problems arise during infancy due to hypotonia, it is followed by hyperphasia that is prone to morbid obesity leading to cardiovascular problems, diabetes, and infectious diseases. And sleep apnea, scoliosis make anesthetic management difficult. We report a case of general anesthetic management during strabismus surgery in a child with Prader-Willi syndrome and its possible considerations.

Keyword

anesthetic management; Prader Willi syndrome

MeSH Terms

Child
Chromosome Aberrations
Communicable Diseases
Humans
Intellectual Disability
Muscle Hypotonia
Obesity, Morbid
Prader-Willi Syndrome*
Scoliosis
Sleep Apnea Syndromes
Strabismus