J Korean Pediatr Soc.  1997 Apr;40(4):567-571.

One Case of Congenital Complete Atrioventricular Block Diagnosed by Fetal Echocardiography

• Kim EJ
• Kang TH
• Lee HD

Abstract

Congenital complete atrioventicular block is uncommon which has a heterogenous etiology. According to recent studies, about one-third of the mothers of the patients who were diagnosed as congenital complete atrioventricular block, had symptoms or signs of connective tissue disease. Even though the outlook is usually regarded as favorable, the mortality is highest in the neonatal period, much lower during childhood and adolescence and increases slowly later in life. In the neonatal period the predominant indication for pacing was heart failure. It is difficult to make a prognosis in the individual patient. A slow, fixed or decreasing venticular rate neonatally and a prolonged QT interval seem to be bad prognostic sign. We report a case of congenital complete atrioventricular block who was diagnosed by fetal echocardiography. Her mother was asymptomatic, but had positive serologic test to anti-Ro antibody and anti-La antibody. We report a case of congenital complete atrioventricular block with a brief review of related literatures.

Keyword

Congenital complete atrioventricular block; Fetal echocardiography; Connective tissue disease

MeSH Terms

Adolescent
Atrioventricular Block*
Connective Tissue Diseases
Echocardiography*
Heart Failure
Humans
Mortality
Mothers
Prognosis
Serologic Tests