J Korean Neurosurg Soc.  2009 Sep;46(3):252-256. 10.3340/jkns.2009.46.3.252.

A Case of Infantile Meningioangiomatosis with a Separate Cyst

• Kim SH
• Yoon SH
• Kim JH

• KMID: 2138415
• DOI: http://doi.org/10.3340/jkns.2009.46.3.252

Abstract

Meningioangiomatosis (MA) is a rare congenital tumor that occurs mostly in 5-15 year old children. There have been only 5 cases previously reported that described the cystic nature within these tumors. We present a case of a MA accompanied by a separate macrocyst. A normally developed 2 year-old female patient presented with partial and generalized seizures. The brain computerized tomogram and magnetic resonance imaging revealed the presence of a calcified mass accompanied by a cyst in the right parietal area, surrounded by low density and high attenuation edema and hemorrhage. Upon right parietal craniotomy, a 1.6 cm x 1.2 cm x 0.5 cm sized plate-like, gray-white, slightly hard mass was seen and it was completely excised. Approximately 1 cm from the mass in the anterior lateral direction, a cyst was found and subsequent biopsy of the cyst wall revealed no tumor tissue, and therefore the cyst was not removed. Pathologic report demonstrated the meningioangiomatosis. Follow up examination 2 years later showed no recurrence of the tumor, and there was no evidence of neurological deficits. Authors suggest that cysts that arise in the surrounding tissues of tumors may not be tumor cysts, and do not require surgical removal.

Keyword

Brain tumor; Cyst; Epilepsy; Infant; Neurofibromatosis

MeSH Terms

Biopsy
Brain
Brain Neoplasms
Child
Craniotomy
Edema
Epilepsy
Female
Follow-Up Studies
Hemorrhage
Humans
Infant
Magnetic Resonance Imaging
Neurofibromatoses
Recurrence
Seizures