Korean J Dermatol.
2006 Jul;44(7):884-886.
A Case of Periumbilical Perforating Pseudoxanthoma Elasticum
- Affiliations
-
- 1Department of Dermatology, College of Medicine, Soonchunhyang University, Seoul, Korea. topdoctor@naver.com
- 2Department of Pathology, College of Medicine, Soonchunhyang University, Seoul, Korea.
Abstract
- Perforating pseudoxanthoma elasticum is a rare disorder. It is an hereditary connective tissue disease involving progressive fragmentation and dystrophic calcification of elastic fibers. The localized lesions usually occur in a periumbilical location in obese, middle-aged, multiparous black women. It is characterized clinically by yellowish, lax, well-circumscribed, reticulated or cobblestoned patches or plaques of the periumbilical region. Herein, we report a case of periumbilical perforating pseudoxanthoma elasticum which occurred in an obese, multiparous woman with no signs of hereditary systemic pseudoxanthoma elasticum.
