Ann Dermatol.
2007 Sep;19(3):139-141. 10.5021/ad.2007.19.3.139.
A Case of Periumbilical Perforating Pseudoxanthoma Elasticum
- Affiliations
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- 1Department of Dermatology, Hanyang University, College of Medicine, Seoul, Korea. romio@hanyang.ac.kr
- KMID: 1520583
- DOI: http://doi.org/10.5021/ad.2007.19.3.139
Abstract
- Periumbilical perforating pseudoxanthoma elasticum is a rare acquired disorder that usually occurs in obese, middle-aged, multiparous women. It is considered as a separate entity from the hereditary pseudoxanthoma elasticum due to lack of hereditary transmission and association with systemic disease. A 70-year-old multiparous woman presented with a 2-year history of a gradually enlarging, yellowish ulcerated plaque in the periumbilical region. The biopsy specimen showed irregularly altered elastic fibers with encrusted calcium salts that underwent transepidermal elimination. We report a rare case of periumbilical perforating pseudoxanthoma elasticum with no signs of hereditary pseudoxanthoma elasticum.
