J Korean Radiol Soc.  2008 Sep;59(3):197-200. 10.3348/jkrs.2008.59.3.197.

Splenic Arteriovenous Malformation Manifestated by Thrombocytopenia in Hereditary Hemorrhagic Telangiectasia: A Case Report

Affiliations
  • 1Department of Radiology, College of Medicine, Dong-A University, Korea.

Abstract

Hereditary hemorrhagic telangiectasia (HHT) is an autosomal dominant inherited disease characterized by epistaxis, telangiectases and visceral arteriovenous malformations (AVMs). The involvement of the gastrointestinal tract, liver, lung and cerebrum for HHT has been described, whereas little is known about AVMs of the spleen. We report here the radiological findings of a case of a splenic AVM manifested by thrombocytopenia in HHT.

Keyword

Spleen; Arteriovenous malformations; Tomography; X-Ray Computed ultrasonography; Telangiectasia; Hereditary hemorrhagic

MeSH Terms

Arteriovenous Malformations
Cerebrum
Epistaxis
Gastrointestinal Tract
Liver
Lung
Spleen
Telangiectasia, Hereditary Hemorrhagic
Telangiectasis
Thrombocytopenia

Cited by  1 articles

Hereditary Hemorrhagic Telangiectasia with Pulmonary and Splenic Arteriovenous Malformation
Mi Hyun Kim, Mee Kyung Namgoong, Young Ju Kim, Soon Hee Jung, Young Uh, Hae Yong Lee
Pediatr Allergy Respir Dis. 2012;22(4):438-443.    doi: 10.7581/pard.2012.22.4.438.

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