J Korean Assoc Oral Maxillofac Surg.  1998 Apr;24(2):241-245.

AGGRESSIVE FIBROMATOSIS OF THE MAXILLA

Affiliations
  • 1Department of Oral & Maxillofacial Surgery, Gachon Medical College, Gil Medical Cener, Korea.
  • 2Department of Pathology, Gachon Medical College, Gil Medical Cener, Korea.

Abstract

Aggressive fibromatosis is best difined as a group of non-encapsulated, non-metastasizing fibrous tumors that have tendency for local recurrence. This tumor is chariaterized histologically by fibroblastic proliferation and clinically by the potential to infiltrate and to recur after surgical excision, but not metastasize. The most common anatomic location have been the abdominal muscle and the extrimities. The incidence of the head and neck is mentioned as from 9.5% to 50% of all desmoid tumors. Within this area, 40%-to 80% of the tumors are located in the neck, but rare in oral cavity. Histologically the tumor is composed of proliferative fibroblasts with a collagenous component. The degree of cellularity varies from area to area and from tumor to tumor. The cells are usually spindle-shaped and the nuclei present only slightly polymorphism, but mitosis are rare and never atypical. Oral fibromatosis has been described as fibrosarcoma, pseusarcoma, pseudosarcomatous fibrosarcoma, metastasizing fibromatosis, juvenile aggressive fibromatosis, and aggressive fibromatosis, but Wilkin and Waldron suggested that the aggressive fibromatosis was a more appropriate term, reflecting the invasive characteristics of the tumor. The treatment of aggressive fibromatosis is traditionally surgical resection with an area of tumor free tissue. But when the complete surgical excision is not possible, radiation and chemotherapy also can be used. Clinically the tumor reported to be not painful in most cases, but capable of rapid growth. Careful clinical and histological examinations are essential for correct diagnosis. We report a case of aggressive fibromatosis. Occurring of the maxilla in 10 year female patient.

Keyword

Aggressive fibromatosis; Complete surgical excision

MeSH Terms

Abdominal Muscles
Collagen
Diagnosis
Drug Therapy
Female
Fibroblasts
Fibroma
Fibromatosis, Aggressive*
Fibrosarcoma
Head
Humans
Incidence
Maxilla*
Mitosis
Mouth
Neck
Recurrence
Collagen
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