Korean J Urol.  2010 Jul;51(7):501-504.

Mesenteric Fibromatosis Causing Ureteral Stenosis

• Choi JY
• Kang KM
• Kim BS
• Kim TH

Abstract

Mesenteric fibromatosis is a rare benign disease characterized by proliferating fibrous tissue in the bowel mesentery. We report a case of aggressive mesenteric fibromatosis with ureteral stenosis arising in a 46-year-old woman who suffered from intermittent right abdominal pain. Computed tomography revealed a right retroperitoneal mass with right ureteral stenosis at the level of the right common iliac vessel. The mass was excised with resection of the affected segment of the ileum, ascending colon, and ureter, and end-to-end ureter anastomosis was performed. Pathological examination confirmed mesenteric fibromatosis.

Keyword

Aggressive fibromatosis; Retroperitoneal neoplasms

MeSH Terms

Abdominal Pain
Colon, Ascending
Constriction, Pathologic*
Female
Fibroma*
Fibromatosis, Aggressive
Humans
Ileum
Mesentery
Middle Aged
Retroperitoneal Neoplasms
Ureter*

Figure

• 

  FIG. 1 Preoperative computed tomography imaging. The contrast-enhanced coronal reformatted image depicts moderate enhancing fibrous tissue (arrow 2) with right ureteral stenosis (arrow 1).

• 

  FIG. 2 Histopathological findings. (A) Grossly, the excised mass was ill-defined and adhered to the small and large intestine (ileocecal valve). (B) Excised ureteral mass. (C) Mesenteric fibromatosis showing cytologically bland spindle cells in a collagenous stroma (H&E, ×200). (D) The cells showed positive nuclear staining for beta-catenin (Immunohistochemical staining, ×200).

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