Obstet Gynecol Sci.  2014 Sep;57(5):412-414. 10.5468/ogs.2014.57.5.412.

Mesenteric desmoid-type fibromatosis causing secondary hypertension in a young woman

• Kim MS
• Noh JH
• Jung MC
• Kim YB

• KMID: 2051726
• DOI: http://doi.org/10.5468/ogs.2014.57.5.412

Abstract

This report describes an 18-year-old woman presenting with abdominal distension, left flank pain, and hypertension. She had a huge abdominal mass, diagnosed as a mesenteric desmoid-type fibromatosis, causing compression of the left external iliac vessels and ureter, as well as elevated renin concentration and hypertension. After surgical removal of the mass, all signs improved including hypertension.

Keyword

Fibromatosis, aggressive; Secondary hypertension

MeSH Terms

Adolescent
Female
Fibroma*
Fibromatosis, Aggressive
Flank Pain
Humans
Hypertension*
Renin
Ureter
Renin

Figure

• 

  Fig. 1 Abdominal computed tomography, showing a huge lobulated mass with heterogeneous attenuation.

• 

  Fig. 2 Cut section with homogeneous appearance and multifocal petechial hemorrhaging.

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