Ewha Med J.  2012 Mar;35(1):49-53. 10.12771/emj.2012.35.1.49.

A Case of Ileal Mesenteric Desmoid Tumor Resected by Laparoscopic Surgery

• Noh KT
• Sung SH
• Lee RA

• KMID: 2134946
• DOI: http://doi.org/10.12771/emj.2012.35.1.49

Abstract

Desmoid tumor is rare neoplasm originated from fibrous sheath or musculoaponeurotic structure. It is classified as benign tumor histologically, but clinically, it has malignant characteristics due to its infiltrative growth to adjacent organ and frequent local recurrence. Especially, mesenteric desmoid tumor shows poor prognosis because of its symptoms of pain, intestinal obstruction, ureter obstruction and fistula formation and high frequency of recurrence. We experienced a case of mesenteric desmoid tumor in a 64-year-old woman with a painless abdominal mass. Laparoscopic exploration was performed and 10 cm sized mesenteric mass was identified, which resected widely and the diagnosis was confirmed with desmoid tumor by pathologic report. We reviewed the feature of the mesenteric desmoid tumor, that is, pathophysiology, clinical presentations, diagnosis, treatment and prognosis.

Keyword

Desmoid tumor; Mesentery; Laparoscopy

MeSH Terms

Female
Fibromatosis, Aggressive
Fistula
Humans
Intestinal Obstruction
Laparoscopy
Mesentery
Prognosis
Recurrence
Ureter

Figure

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  Fig. 1 Abdominal CT findings. 10×6.5 cm sized solid mass is visible in right lower quadrant. The tumor originates from small bowel mesentery. (A) Horizontal view. (B) Coronal view.

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  Fig. 2 Gross pathologic finding. 9.5×9×5 cm sized well demarcated mass is identified in the small bowel mesentery. Retraction diverticulum is visible on ileal mucosa.

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  Fig. 3 Micropathologic finding. (A) The tumor infiltrates into the muscle layers of small bowel (H&E stain, ×40). (B) Fibroblastic spindle cells are arranged orderly in collagenous or myxoid matrix (H&E stain, ×100).

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  Fig. 4 Immunohistochemical stain for β-catenin shows nuclear and cytoplasmic positivity in tumor cells (Immunohistochemical stain, ×400).

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