- A Case of Desensitization for Hemophilia B Inhibitor Patient with Anaphylaxis to FIX Concentrates
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Park Y, Yoo KY
- KMID: 2252186
- Korean J Hematol.
- 2008 Sep;43(3):179-183.
- doi: 10.5045/kjh.2008.43.3.179
Among the patients with hemophilia, 10~15% have hemophilia B, and 1~3% of the hemophilia B patients develop inhibitor to factor IX clotting activity. Allergic reactions to concentrates containing factor IX... -
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- Gene Therapy in Rats with a Lentiviral Vector Containing the Human Coagulation Factor IX Gene
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Kim ST, Oh T, Jeon HJ, Kim OH, Lee SM
- KMID: 1477826
- Korean J Blood Transfus.
- 2008 Apr;19(1):1-8.
BACKGROUND: Hemophilia B is an inheritable X-linked bleeding disorder that occurs as a consequence of genetic alterations within the factor IX (IX) gene. In the present study, pseudotyped HIV-I-derived lentiviral... -
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- Anesthetic Management of a Patient with Hemophilia B
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Lee HJ, Jun JH, Kim KH, Seung IS, Ryu JH
- KMID: 2236709
- Korean J Anesthesiol.
- 2004 Mar;46(3):376-377.
- doi: 10.4097/kjae.2004.46.3.376
A 22 year old male with hemophilia B was scheduled for the correction of a right subtrochanteric femur fracture. Plasma concentration of coagulation factor IX in this patient was 50%... -
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- A Case of Hemophilia B Diagnosed after Rhinosinus Surgery in 37 Year-Old Patient
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Kim HD, Choi IS
- KMID: 2436473
- Korean J Otorhinolaryngol-Head Neck Surg.
- 2018 Jun;61(6):308-311.
- doi: 10.3342/kjorl-hns.2016.17489
Hemophilia is an X-linked recessive disorder, which is classified into hemophilia A, defined by factor VIII deficiency and hemophilia B, defined by factor IX deficiency. The usual clinical presentation is... -
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- Recurrent Cerebral Venous Thrombosis Associated with Elevated Factor VIII
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Kim MJ, Cho AH, No YJ, Kim HY, Kim JS
- KMID: 1980473
- J Clin Neurol.
- 2006 Dec;2(4):286-289.
- doi: 10.3988/jcn.2006.2.4.286
Cerebral venous thrombosis (CVT) rarely recurs, and the factors associated with a recurrence remain unclear. Recently, however, elevated plasma coagulation factor VIII has been considered a factor related to recurrent... -
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- Usefulness of HhaI and MseI DNA Polymorphism of Factor IX Gene in the Molecular Genetic Diagnosis of Hemophilia B in Korean Population
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Lee JH, Choi YM, Choe J, Hwang DY, Lee JY
- KMID: 2261608
- Korean J Obstet Gynecol.
- 1999 Dec;42(12):2761-2767.
OBJECTIVES: Hemophilia B has been known to result from more than 500 kinds of mutations. And it is difficult to find out a mutation specific for each family. Therefore, linkage... -
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- Recent Advance of Pharmacotherapy in Hemophilia
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Park YS
- KMID: 2188133
- J Korean Med Assoc.
- 2009 Dec;52(12):1201-1206.
- doi: 10.5124/jkma.2009.52.12.1201
Hemophilia A (factor VIII deficiency) and Hemophilia B (factor IX deficiency) are the most common and serious congenital coagulation disorders. Accurate diagnosis is important and essential for effective management. A... -
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- Iliacus Hematoma with Femoral Neuropathy in Hemophilia: A Case report
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Choi HY, Lee JH, Choi ST, Kim NS, Kim CJ, Yu HC
- KMID: 2423685
- J Korean Orthop Assoc.
- 1996 Aug;31(4):904-908.
- doi: 10.4055/jkoa.1996.31.4.904
Hemophilia, a genetically determined disorder, can be divided into hemophilia A and hemophilia B. Hemophilia A, defined as a sex-linked recessive trait hemorrhagic disease of males characterized by a deficiency... -
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- The activity of factor VIII and IX of cord blood at mid-trimester in fetuses without hemophilia
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Choe DK, Oh JW, Jun JK, Choi YM
- KMID: 2369025
- J Genet Med.
- 2016 Dec;13(2):89-94.
- doi: 10.5734/JGM.2016.13.2.89
PURPOSE: Molecular genetic analysis is the main approach used for prenatal diagnosis of hemophilia A and B. However, in certain cases, such analysis is uninformative. In such situations, direct measurement... -
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- A Case of Repeated Cesarean Section on the Patient who has a Moderate Hemophilia B
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Lee DN, Oh YJ, Kyung YS, Yoon SW, Choi JS, Kim KH, Lee KW, Kim SD, Han JS
- KMID: 2272211
- Korean J Obstet Gynecol.
- 2003 Nov;46(11):2317-2322.
Hemophilia is a hemorrhagic disease caused by the defect or abnormal activities of the coagulation factor. The proper dosage and interval of factor replacement therapy are not defined. So the... -
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- A Study for Changes of blood clotting factor during Hormone Replacement Therapy of Postmenopausal woman
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Lee G, Jung H
- KMID: 2075715
- Korean J Obstet Gynecol.
- 1999 Apr;42(4):790-794.
OBJECTIVE: To evaluate the effect of HRT using estrogen combined with progesterone on the coagulation system. METHOD: A total of 60 patients who visited menopausal clinic of Obstetrics and Gynecology... -
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- A Case of Heel Reconstruction with a Reverse Sural Artery Flap in a Hemophilia B Patient
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Lee BK, Shim JS
- KMID: 1921079
- Arch Plast Surg.
- 2012 Mar;39(2):150-153.
- doi: 10.5999/aps.2012.39.2.150
Hemophilia B is a rare blood coagulation disorder. Complications such as bleeding and hematoma can cause necrosis of flaps, wound disruption, and the disturbance of wound healing. In particular, guidelines... -
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- Human coagulation factor VIII domain-specific recombinant polypeptide expression
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Choi SJ, Jang KJ, Lim JA, Kim HS
- KMID: 2172774
- Blood Res.
- 2015 Jun;50(2):103-108.
- doi: 10.5045/br.2015.50.2.103
BACKGROUND: Hemophilia A is caused by heterogeneous mutations in F8. Coagulation factor VIII (FVIII), the product of F8, is composed of multiple domains designated A1-A2-B-A3-C1-C2. FVIII is known to interact... -
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- Moderate Hemophilia B Diagnosed by Massive Gastrointestinal Hemorrhage on the First Day of Life: A Case Report and Literature Review
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Park SH, Choe BH
- KMID: 2360465
- Neonatal Med.
- 2016 Nov;23(4):238-241.
- doi: 10.5385/nm.2016.23.4.238
Gastrointestinal hemorrhage in neonates is commonly associated with necrotizing enterocolitis, cow's milk protein allergy, and gastrointestinal malformation. Gastrointestinal bleeding on the first day of life, presenting as the first manifestation... -
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- RFLP Analysis of a Gene for Blood Coagulation Factor IX in Korean
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Kwon M, Lee JM, Jeon BK, Oh SG, Ryou CS, Oh BH
- KMID: 2076196
- Korean J Obstet Gynecol.
- 2001 Mar;44(3):506-512.
OBJECTIVE: The purpose of this study was to investigate the methods for analysis of restriction fragment length polymorphisms of hemophilia B (coagulation factorIX) gene in Korean population. METHODS: Genomic DNAs... -
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- A Case of Cerebral Infarction in a Child with Acute Lymphoblastic Leukemia Developed during Chemotherapy with E coli Asparaginase
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Oh JH, Cho HS, Han SW, Park CY
- KMID: 2037445
- Korean J Pediatr Hematol Oncol.
- 2000 Oct;7(2):305-309.
E. coli L-asparaginase treatment during induction therapy in acute lymphoblastic leukemia is known to be rarely complicated by thromboembolic events. It causes deficiencies of antithrombin III, plasminogen, fibrinogen, factor... -
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- The prevalence and risk factors of inhibitor development of FVIII in previously treated patients with hemophilia A
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Kim JY, You CW
- KMID: 2459386
- Blood Res.
- 2019 Sep;54(3):204-209.
- doi: 10.5045/br.2019.54.3.204
BACKGROUND: Risk factors for the development of inhibitors in previously untreated patients (PUPs) have been reported; this is not the case in previously treated patients (PTPs) owing to fewer studies.... -
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- Global hemostatic assay of different target procoagulant activities of factor VIII and factor IX
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Yoo KY, Jung SY, Hwang SH, Lee SM, Park JH, Nam HJ
- KMID: 2414363
- Blood Res.
- 2018 Mar;53(1):41-48.
- doi: 10.5045/br.2018.53.1.41
BACKGROUND: Korean National Health Insurance reimburses factor VIII (FVIII) and factor IX (FIX) clotting factor concentrate (CFC) infusions to discrepant activity levels, allowing elevation of FVIII activity to 60 IU/dL... -
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- Dental Treatment of Child with Hemophilia
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Lim JE, Lee SE, Ahn HJ, Park JH, Choi SC
- KMID: 2345037
- J Korean Dent Soc Anesthesiol.
- 2012 Dec;12(4):229-233.
- doi: 10.17245/jkdsa.2012.12.4.229
Hemophilia, the most common of the inherited bleeding disorder, is the result of a deficiency of clotting factor. Since bleeding after dental treatment may cause severe or even fatal complications,... -
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- Perioperative Management of Patients with Hemophilia during Spinal Surgery
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Kobayashi , Imagama S, Ando K, Ito K, Tsushima M, Morozumi M, Tanaka S, Machino M, Ota K, Nishida Y, Ishiguro N
- KMID: 2430658
- Asian Spine J.
- 2018 Jun;12(3):442-445.
- doi: 10.4184/asj.2018.12.3.442
STUDY DESIGN: Single-center retrospective study. PURPOSE: To optimize the perioperative management of patients with hemophilia who are undergoing spinal surgery. OVERVIEW OF LITERATURE: Hemophilia is a rare disease in which there is... -
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