Res Vestib Sci.  2023 Sep;22(3):83-88. 10.21790/rvs.2023.22.3.83.

A Case of Patient with Bilateral Cochleovestibular Function Loss due to Infratentorial Superficial Siderosis

• Lee G
• Mun Y
• Shim DB

• KMID: 2545899
• DOI: http://doi.org/10.21790/rvs.2023.22.3.83

Abstract

Superficial siderosis (SS) is a rare neurodegenerative condition characterized by hemosiderin deposition in the central nervous system, which sometimes leads to sensorineural hearing loss and vestibular dysfunction. This case report details the diagnosis and treatment of a 63-year-old female patient presenting with a yearlong history of postural instability and recent symptoms of sudden right-sided hearing loss and imbalance. Physical examination and imaging revealed bilateral deafness and infratentorial SS. Treatment, including medication, vestibular exercises, high-dose steroids, and hyperbaric oxygen therapy, led to a significant alleviation of dizziness but no improvement in hearing. This case emphasizes the need for clinicians to consider SS in patients presenting with sudden-onset hearing loss and dizziness, even without prior any medical history or trauma, to accurately identify the underlying cause.

Keyword

Superficial siderosis; Bilateral vestibulopathy; Hearing loss; Vertigo; 표재철침착증; 전정장애; 청력 손실; 현훈