Investig Magn Reson Imaging.  2020 Mar;24(1):51-54. 10.13104/imri.2020.24.1.51.

A Case of Idiopathic Infratentorial Superficial Siderosis

• Shin Du
• Yang SY
• Kim Yw
• Ryu HS
• Lee H

• KMID: 2508218
• DOI: http://doi.org/10.13104/imri.2020.24.1.51

Abstract

Superficial siderosis is attributed to hemosiderin deposition in the subpial layers of the nervous system. The clinical features of infratentorial superficial siderosis (ISS) are hearing loss, cerebellar ataxia, and corticospinal tract signs and the most common cause of idiopathic ISS is a dural defect. As magnetic resonance imaging (MRI) has advanced, the diagnosis of infratentorial superficial siderosis can be confirmed by unique radiological findings in MRI. Here, we report on a female patient diagnosed with idiopathic ISS by means of clinical symptoms and radiological findings.

Keyword

Superficial siderosis; Hearing loss; Cerebellar ataxia

Figure

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  Fig. 1. Idiopathic infratentorial superficial siderosis. Brain magnetic resonance imaging (MRI) (a-c) and spine MRI (km) show low signal intensities in the cerebrum, cerebellum, brain stem, and spinal cord in T2-weighted images and the corresponding T2∗-weighted gradient-recalled echo (GRE) images (d-f) or susceptibility-weighted images (SWI) (g-i) show low signal intensities in the same regions, which suggest a typical hemosiderin deposition pattern. The “blooming” effect on the SWI (h, arrowhead) is more remarkable compared to that on the T2-weighted GRE images (e, asterisk). Spine MRI (j-m) shows cerebrospinal fluid collection (arrows).

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