J Korean Neurol Assoc.  2018 Aug;36(3):189-191. 10.17340/jkna.2018.3.9.

Symptomatic Relief of Idiopathic Infratentorial Superficial Siderosis with Maintaining Supine Position

• Jo S
• Ko MA
• Lee D
• Kwon HS
• Kwon SU

• KMID: 2436075
• DOI: http://doi.org/10.17340/jkna.2018.3.9

Abstract

Superficial siderosis results from the deposition of hemosiderin in subpial layers of the central nervous system following hemorrhage in subarachnoid spaces. Infratentorial superficial siderosis (ISS) presents with unique clinical features including progressive hearing loss, ataxia, and myelopathy, and the most common cause of idiopathic ISS is dural abnormality. Here we report a case of idiopathic ISS with radiological findings of spontaneous intracranial hypotension, whose clinical symptoms of ISS including cerebellar dysfunction improved after supine position was maintained for 2 months.

Keyword

Siderosis; Subdural effusion; Intracranial hypotension

MeSH Terms

Ataxia
Central Nervous System
Cerebellar Diseases
Hearing Loss
Hemorrhage
Hemosiderin
Intracranial Hypotension
Siderosis*
Spinal Cord Diseases
Subarachnoid Space
Subdural Effusion
Supine Position*
Hemosiderin