Korean J Thorac Cardiovasc Surg.
2018 Jun;51(3):223-226. 10.5090/kjtcs.2018.51.3.223.
Erdheim-Chester Disease Presenting as an Anterior Mediastinal Tumor without Skeletal Involvement
- Affiliations
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- 1Department of Thoracic and Cardiovascular Surgery, Korea University Guro Hospital, Korea University College of Medicine, Korea.
- 2Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine, Korea. scena@dreamwiz.com
- 3Department of Pathology, Asan Medical Center, University of Ulsan College of Medicine, Korea.
- KMID: 2413067
- DOI: http://doi.org/10.5090/kjtcs.2018.51.3.223
Abstract
- Erdheim-Chester disease (ECD) is a form of non-Langerhans cell histiocytosis that most commonly involves the skeletal system. We report an unusual case of ECD presenting as an anterior mediastinal tumor without skeletal involvement. A 60-year-old man with no remarkable medical history was referred for evaluation of a mediastinal mass. The patient underwent surgical excision of the tumor via video-assisted thoracoscopic surgery. Histologic examination revealed marked proliferation of atypical histiocytes with sclerosis, and the results of immunohistochemical staining were suggestive of ECD.
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