J Korean Soc Radiol.
2023 May;84(3):757-762. 10.3348/jksr.2022.0114.
Erdheim–Chester Disease Involving the Biliary System and Mimicking Immunoglobulin G4-Related Disease: A Case Report
- Affiliations
-
- 1Department of Radiology, Seoul Medical Center, Seoul, Korea
- 2Department of Radiology, Severance Hospital, Yonsei University College of Medicine, Seoul, Korea
- KMID: 2542914
- DOI: http://doi.org/10.3348/jksr.2022.0114
Abstract
- First described in 1930 as a lipoid granulomatosis, Erdheim-Chester disease (ECD) is a rare histiocytosis encompassing a group of disorders caused by overproduction of histiocytes, a subtype of white blood cells. This disease most commonly involves the bones and can affect organs in the abdomen; however, biliary involvement is rarely reported. We report a case of ECD with biliary involvement, which rendered it difficult to radiologically distinguish ECD from immunoglobulin G4-related disease.
- Full Text Links
-
- Actions
-
Cited
- CITED
-
- Close
- Share
-
- Similar articles
-
- Erdheim-Chester Disease with Perirenal Masses Containing Macroscopic Fat Tissue
- Commentary on "A Case of Erdheim-Chester Disease with Asymptomatic Renal Involvement"
- A Case of Erdheim-Chester Disease Mimicking Systemic Lymphangitic Metastasis
- Mass-Forming Immunoglobulin G4-Related Ampullitis Mimicking a Duodenal Subepithelial Tumor: A Case Report
- Erdheim-Chester Disease Involving Lymph Nodes and Liver Clinically Mimicking Lymphoma: A Case Report
