Korean J Med.
2011 Jun;80(6):712-717.
A Case of Erdheim-Chester Disease Mimicking Systemic Lymphangitic Metastasis
- Affiliations
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- 1Department of Internal Medicine, Ewha Womans University School of Medicine, Ewha Medical Research Institute, Seoul, Korea. hs1017@ewha.ac.kr
- 2Department of Pathology, Ewha Womans University School of Medicine, Ewha Medical Research Institute, Seoul, Korea.
Abstract
- Erdheim-Chester disease (ECD) is non-Langerhans cell histiocytosis that leads to multi-organ involvement with unknown etiology. We report a 64-year-old woman with a dry cough and dyspnea. She had interlobular septal thickening and ground-glass opacity in both lungs, suggesting lymphangitic lung metastasis. However, she was diagnosed with ECD after a long bone and immunohistological evaluation.