J Korean Assoc Pediatr Surg.  2017 Dec;23(2):59-61. 10.13029/jkaps.2017.23.2.59.

A Case Report of Gardner-Associated Fibroma in 19-Month-Old Girl

• Lee H
• Han JW
• Youn JK
• Kim HY

• KMID: 2398579
• DOI: http://doi.org/10.13029/jkaps.2017.23.2.59

Abstract

Gardner-associated fibroma (GAF) is a benign lesion of soft tissue which has recently been described and is exceedingly rare in children. GAF is associated with adenomatous polyposis coli gene mutation, familial adenomatous polyposis and desmoid. We report a case of patient with soft tissue tumor on her lower back which was turned out to be GAF. The patient was a 19-month-old female who visited out-patient clinic with palpable mass on her lower back and we performed surgical excision. The tumor was located at subcutaneous and we excised the tumor including surrounding soft tissue. She discharged without any complication on surgery day. The pathologic report showed dense collagenous tissue with spindle cell and adipose tissue, suggestive of GAF. We are planning to check gene study and to perform endoscopy and abdominal ultrasonography for at the age of 4.

Keyword

Gardner syndrome; Fibroma; Adenomatous polyposis coli; Children

MeSH Terms

Adenomatous Polyposis Coli
Adipose Tissue
Child
Collagen
Endoscopy
Female*
Fibroma*
Fibromatosis, Aggressive
Gardner Syndrome
Humans
Infant*
Outpatients
Ultrasonography
Collagen

Figure

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  Fig. 1 Ultrasound finding of lesion (arrows).

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  Fig. 2 Gross picture of specimen; the specimen was divided into several pieces and the size of biggest one was 1.5×1.3×0.4 cm.

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  Fig. 3 Microscopic finding of specimen; dense collagenous tissue with balnd spindle cells and adipose tissue (H&E, ×40).

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