Vasc Spec Int.  2017 Sep;33(3):112-116. 10.5758/vsi.2017.33.3.112.

Sequential Hybrid Repair of Aorta and Bilateral Common Iliac Arteries Secondary to Chronic Aortic Dissection with Extensive Aneurysmal Degeneration in a Marfan Patient

• Hinojosa C
• Anaya-Ayala JE
• Laparra-Escareno H
• Lizola R
• Torres-Machorro A

• KMID: 2396191
• DOI: http://doi.org/10.5758/vsi.2017.33.3.112

Abstract

Marfan syndrome is a connective tissue disorder associated with aortic dissection, aneurysmal degeneration and rupture. These cardiovascular complications represent the main cause of mortality, therefore repair is indicated. We present a 35-year-old woman who experienced acute onset of chest pain. Her imaging revealed a chronic DeBakey type I dissection with aortic root dilation and descending thoracic aneurysmal degeneration. She underwent a Bentall procedure and endovascular exclusion of the descending thoracic aortic aneurysm. She was closely followed and 2 years later a computed tomography angiography (CTA) revealed the aneurysmal degeneration of the thoracoabominal aorta and bilateral iliac arteries. The patient underwent a composite reconstruction using multi-visceral branched and bifurcated Dacron grafts. At 5 years from her last surgery, a CTA revealed no new dissection or further aneurysmal degenerations. Aortic disease in Marfan patients is a complex clinical problem that may lead to secondary or tertiary aortic reconstructions; close follow-up is mandatory.

Keyword

Marfan syndrome; Chronic aortic dissection; Aneurysmal degeneration; Hybrid repair

MeSH Terms

Adult
Aneurysm*
Angiography
Aorta*
Aortic Aneurysm, Thoracic
Aortic Diseases
Chest Pain
Connective Tissue
Female
Follow-Up Studies
Humans
Iliac Artery*
Marfan Syndrome
Mortality
Polyethylene Terephthalates
Rupture
Transplants
Polyethylene Terephthalates