Korean J Thorac Cardiovasc Surg.  2018 Feb;51(1):61-63. 10.5090/kjtcs.2018.51.1.61.

Minimally Invasive Mitral Valve Repair in a Woman with Marfan Syndrome and Type B Dissection

• Lim MH
• Je HG
• Lee SK

• KMID: 2409715
• DOI: http://doi.org/10.5090/kjtcs.2018.51.1.61

Abstract

We report the case of a patient with mitral regurgitation complicated by type B dissection and Marfan syndrome (MFS) who was managed successfully with minimally invasive mitral valve repair. Without type A aortic dissection or aortic root dilation, MFS patients may develop mitral valve regurgitation, as in this case, and need valve surgery to improve their symptoms and long-term survival. However, it is not clear that a full sternotomy and prophylactic aortic surgery are necessary. Although retrograde perfusion to the dissected aorta is controversial, our approach minimizes the risk of future anticipated aortic surgery in MFS patients.

Keyword

Minimally invasive surgical procedures; Mitral valve annuloplasty; Aortic dissection; Marfan syndrome

MeSH Terms

Aorta
Female
Humans
Marfan Syndrome*
Minimally Invasive Surgical Procedures
Mitral Valve Annuloplasty
Mitral Valve Insufficiency
Mitral Valve*
Perfusion
Sternotomy