Yeungnam Univ J Med.  1989 Jun;6(1):179-184. 10.12701/yujm.1989.6.1.179.

A Case of Dissection in Marfan Syndrome with Ascending Aortic Aneurysm

Abstract

The Marfan syndrome is a generalized connective tissue disease involving eye, musculoskeletal system, cardiovascular system, and inherited autosomal dominant with various expression type. The cardiovascular complications such as aortic aneurysm, aortic dissection, aortic regurgitation, mitral regurgitation and aortic dissection which usually occurs in previously normal sized aorta are poor prognostic factors. However, the aortic dissection which developed in patient with Marfan syndrome and aortic aneurysm was rare. We experienced one case of dissecting aneurysm in patient diagnosed as previous aortic aneurysm, aortic regurgitation, and Marfan syndrome, receiving successful operation.


MeSH Terms

Aneurysm, Dissecting
Aorta
Aortic Aneurysm*
Aortic Valve Insufficiency
Cardiovascular System
Connective Tissue Diseases
Humans
Marfan Syndrome*
Mitral Valve Insufficiency
Musculoskeletal System
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