J Dent Anesth Pain Med.  2016 Dec;16(4):313-316. 10.17245/jdapm.2016.16.4.313.

Perioperative airway management of a patient with Beckwith-Wiedemann syndrome

• Tsukamoto
• Hitosugi T
• Yokoyama T

• KMID: 2366161
• DOI: http://doi.org/10.17245/jdapm.2016.16.4.313

Abstract

Airway obstruction in pediatric patients always poses a challenge for anesthesiologists. Beckwith-Wiedemann syndrome causes various abnormalities such as macroglossia and omphalocele. Patients with these abnormalities often need corrective surgeries. Management of difficult airway caused by conditions such as macroglossia in patients with this syndrome could be challenging. We encountered a case of difficult airway in an infant with Beckwith-Wiedemann syndrome. It was predicted that macroglossia might cause difficult ventilation, intubation, and extubation. Preoperative assessment and preparations for difficult airway should be considered.

Keyword

Airway management; Beckwith-Wiedemann syndrome; General anesthesia

MeSH Terms

Airway Management*
Airway Obstruction
Anesthesia, General
Beckwith-Wiedemann Syndrome*
Hernia, Umbilical
Humans
Infant
Intubation
Macroglossia
Ventilation

Figure

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  Fig. 1 Macroglossia in the patient with Beckwith-Wiedemann syndrome after intubation.

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