Korean J Urol.  1996 Dec;37(12):1417-1420.

Testicular Yolk Sac Tumor in Beckwith-Wiedemann Syndrome

• Park BJ
• Jeong IY
• Ro DW
• Kim DY
• Park JS

Abstract

The Beckwith-Wiedemann syndrome, which included congenital anomalies such as macroglossia, exomphalos, postnatal somatic gigantism, have a substantially increased risk for the development of tumor. We report a case of testicular yolk sac tumor associated with Beckwith-Wiedemann syndrome, a previously unreported association. Pathologic examination showed Schiller-Duval body with evidence of testicular yolk sac tumor. This finding appears to represent a previously unreported association between Beckwith-Wiedemann syndrome and testicular yolk sac tumor.

Keyword

yolk sac tumor; testis; Beckwith-Wiedemann syndrome

MeSH Terms

Beckwith-Wiedemann Syndrome*
Endodermal Sinus Tumor*
Gigantism
Hernia, Umbilical
Macroglossia
Testis
Yolk Sac*