Korean J Anesthesiol.  2009 May;56(5):583-586. 10.4097/kjae.2009.56.5.583.

Anesthetic management of children with Beckwith-Wiedemann syndrome : Two cases report

Affiliations
  • 1Department of Anesthesiology and Pain Medicine, Seoul National University College of Medicine, Seoul, Korea. kimjintae73@dreamwiz.com

Abstract

Beckwith-Wiedemann syndrome consists of various abnormalities, including macroglossia, visceromegaly, omphalocele, and neonatal hypoglycemia. These abnormalities frequently require operative correction and careful anesthetic management. Principal problems associated with anesthetic management in this syndrome are congenital heart disease, hypoglycemia, and difficult airway combined with macroglossia. We report two cases of general anesthetic management in children with Beckwith-Wiedemann syndrome.

Keyword

Anesthesia; Beckwith-Wiedemann syndrome; Glossectomy; Hypoglycemia; Macroglossia

MeSH Terms

Anesthesia
Beckwith-Wiedemann Syndrome
Child
Glossectomy
Heart Diseases
Hernia, Umbilical
Humans
Hypoglycemia
Macroglossia
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