Ann Dermatol.  1990 Jan;2(1):17-20. 10.5021/ad.1990.2.1.17.

Erythrokeratodermia Variabilis with Alopecia Universalis

• Lee JS
• Sung YH
• Lee JH
• Park JK

• KMID: 2362051
• DOI: http://doi.org/10.5021/ad.1990.2.1.17

Abstract

We describe a 8-year-old girl with erythrokeratodermia varibilis (EKV). This diagnosis was supported by erythematous, configurate patches over the entire body. Their size, shape and location varyed with enviromental factors and emotional state. In addition, well defined brownish, hyperkeratotic plaques were scattered over the trunk and extremities. Also, this patient had alopecia universalis, which is not typical of EKV. Etretinate therapy resulted in an almost complete clinical clearing of the plaques; however, her alopecia universalis and erythematous lesions were not affected.

Keyword

Alopecia universalis; Erythrokeratodermia variabilis; Etretinate; Ichthyosiform dermatosis

MeSH Terms

Acitretin
Alopecia*
Child
Diagnosis
Erythrokeratodermia Variabilis*
Etretinate
Extremities
Female
Humans
Acitretin
Etretinate