J Korean Ophthalmol Soc.  2012 Jun;53(6):861-865.

A Case of Congenital Eyelid Retraction

• Lee S
• Ahn M

Abstract

PURPOSE
To report a case of congenital eyelid retraction with eyelid asymmetry.
CASE SUMMARY
12-year-old male patient visited our clinic with eyelid asymmetry, which had found 6 months after birth. On examination, his marginal reflex distance (MRD1) was 4.0 mm for right eye, and 7.5 mm for left eye. There was no significant notice from orbital computed tomography or laboratory findings and other factors that might have caused eyelid retraction were not found. As treatment, Botulinum toxin type A was injected under the upper tarsal conjunctiva. The upper eyelid retraction was relieved to MRD1 = 4.0 mm after 1 week and MRD1 = 5.5 mm after 1 month. This case was diagnosed as congenital eyelid retraction of upper eyelid.
CONCLUSIONS
Diagnosis of congenital eyelid retraction should be considered to patients with eyelid asymmetry, and the symptom can be relieved with Botulinum toxin type A injection.

Keyword

Botulinum toxin type A; Congenital eyelid retraction

MeSH Terms

Botulinum Toxins, Type A
Child
Conjunctiva
Eye
Eyelids
Humans
Male
Orbit
Parturition
Reflex
Botulinum Toxins, Type A

Figure

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  Figure 1 The child showed left eyelid retraction, 6 years ago (A). The patient shows upper eyelid retraction on examination (B).

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  Figure 2 Photographs of 9 cardinal gazes on examination. No limitation of eyeball movement.

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  Figure 3 Axial (A) and coronal (B) CT images show no evidence of abnormalities.

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  Figure 4 Upper eyelid retraction in the left eye (A) before botulinum toxin injection. (B) One week after botulinum toxin injection. (C) One month after botulinum toxin injection.

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