J Korean Pediatr Soc.  2002 May;45(5):664-668.

Hemophagocytic Syndrome with Kawasaki Disease and Peripheral Gangrene

• Yun HJ
• Jeon KW
• Kim HM
• Park SW
• Uh Y

Abstract

A twenty six months-old boy developed hemophagocytic syndrome during the course of Kawasaki disease. Despite the appropriate treatment modalities for Kawasaki disease, he developed thrombocytopenia, hepatomegaly, high-grade fever, hypertriglyceridemia, peripheral gangrene, and evidence of hemophagocytosis in bone marrow biopsy. Although the course was stormy, he responded well to a combination therapy of corticosteroid and etoposide.

Keyword

Etoposide; Hemophagocytic syndrome; Bone marrow biopsy; Kawasaki disease; Peripheral gangrene

MeSH Terms

Biopsy
Bone Marrow
Etoposide
Fever
Gangrene*
Hepatomegaly
Humans
Hypertriglyceridemia
Lymphohistiocytosis, Hemophagocytic*
Male
Mucocutaneous Lymph Node Syndrome*
Thrombocytopenia
Etoposide