J Korean Soc Pediatr Nephrol.  2009 Oct;13(2):271-277.

A Case about Cyclosporine Treatment of Kimura's Disease Associated with Steroid Dependant Nephrotic Syndrome

• Do YS
• Kim HY
• Namgoong M

Abstract

Kimura's disease is a chronic inflammatory disorder of unknown etiology. A 14 year old boy suffering from steroid dependant nephrotic syndrome, was presented with relapsing painless subcutaneous masses on the left buccal area. Blood analysis showed increased IgE and eosinophilia. During 4 years follow up, he was been treated by low dose steroid and short term cyclosporine. Consequently, frequent relapses of subcutaneous masses and nephrotic syndrome has been relieved. Cyclosporine treatment combined with steroid may be useful for preventing frequent relapse of Kimura's disease.

Keyword

Kimura's disease; Steroid dependant nephrotic syndrome; Cyclosporine

MeSH Terms

Cyclosporine
Eosinophilia
Follow-Up Studies
Immunoglobulin E
Nephrotic Syndrome
Recurrence
Stress, Psychological
Cyclosporine
Immunoglobulin E