Korean J Med.
1998 Jun;54(6):867-872.
A Case of diffuse dilatated coronary artery ectasia on Marfan's Syndrome
- Affiliations
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- 1Department of Internal Medicine, Kangbuk Samsung Hospital, Collage of Medicine, Sungkyunkwan, Seoul, Korea.
- 2Department of Chest Surgery, Kangbuk Samsung Hospital, Collage of Medicine, Sungkyunkwan, Seoul, Korea.
- 3Department of Pathology, Kangbuk Samsung Hospital, Collage of Medicine, Sungkyunkwan, Seoul, Korea.
Abstract
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Marfan's syndrome is a an autosomal dominant disorder of connective tissue that is characterized by ocular, skeletal, and cardiovascular manifestation. It is estimated to have a prevalence of 4-6 per 10,000 people, and at least 25 percent of the cases occur in the absence of a family history. Coronary artery ectasia is a diffuse abnormality of the vessel wall, which has been reported in associated with coronary atherosclerosis, infectious process, congenital heart lesion, syphilis, Ehlers-Danlos syndrome. We reported a case of 25-year-old male who presented with Marfan's syndrome associated with dissecting ascending arotic aneurysm and diffuse dilatated coronary artery ectasia. Coronary angiographic study demonstrated the diffusely dilatated coronary artery ectasia.