Korean J Med.  1998 Jun;54(6):867-872.

A Case of diffuse dilatated coronary artery ectasia on Marfan's Syndrome

Affiliations
  • 1Department of Internal Medicine, Kangbuk Samsung Hospital, Collage of Medicine, Sungkyunkwan, Seoul, Korea.
  • 2Department of Chest Surgery, Kangbuk Samsung Hospital, Collage of Medicine, Sungkyunkwan, Seoul, Korea.
  • 3Department of Pathology, Kangbuk Samsung Hospital, Collage of Medicine, Sungkyunkwan, Seoul, Korea.

Abstract

Marfan's syndrome is a an autosomal dominant disorder of connective tissue that is characterized by ocular, skeletal, and cardiovascular manifestation. It is estimated to have a prevalence of 4-6 per 10,000 people, and at least 25 percent of the cases occur in the absence of a family history. Coronary artery ectasia is a diffuse abnormality of the vessel wall, which has been reported in associated with coronary atherosclerosis, infectious process, congenital heart lesion, syphilis, Ehlers-Danlos syndrome. We reported a case of 25-year-old male who presented with Marfan's syndrome associated with dissecting ascending arotic aneurysm and diffuse dilatated coronary artery ectasia. Coronary angiographic study demonstrated the diffusely dilatated coronary artery ectasia.

Keyword

Marfan's syndrome; Coronary artery ectasia

MeSH Terms

Adult
Aneurysm
Connective Tissue
Coronary Artery Disease
Coronary Vessels*
Dilatation, Pathologic*
Ehlers-Danlos Syndrome
Heart
Humans
Male
Marfan Syndrome*
Prevalence
Syphilis
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