Korean J Dermatol.
1998 Aug;36(4):712-716.
A case of Proteus Syndrome with Characteristic Clinical Manifestations
- Affiliations
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- 1Department of Dermatology, Korea Veternas Hospital, Korea.
- 2Department of Pathology, Chung-Ang University, College of Medicine, Seoul, Korea.
Abstract
- The term Proteus syndrome was coined in 1983 to describe a disorder of skeletal, hamartoinatous and other mesodermal malformations. The syndrome was named after the Greek god Proteus, whose name means "the Polymorphous". Major manifestations are hemihypertrophy, macrodactyly, exostoses, epidermal nevi, characteristic cerebriform masses involving the plantar or palmar surfaces, a variety of subcutaneous masses and scoliosis. We report a 12-year-old boy with Proteus syndrome who had the unique features of this syndrome.
