Korean J Anesthesiol.  2005 Feb;48(2):211-215. 10.4097/kjae.2005.48.2.211.

Anesthetic Management of a Patient with Proteus Syndrome: A case report

• Choi WJ
• Shin HK
• Kang WJ

• KMID: 2238389
• DOI: http://doi.org/10.4097/kjae.2005.48.2.211

Abstract

Proteus syndrome is a rare condition that can be loosely categorized as a hamartomatous disorder. It is a complex disorder with multisystem involvement and great clinical variability. At this time, it is unknown how many individuals have Proteus syndrome, since not all cases of Proteus syndrome are documented. We do not know whether anesthetic problems in Proteus syndrome are common or not, but as there is a high incidence of cervical spine involvement, we anticipate significant anesthetic problems. We experienced such a case under general anesthesia for liposuction to lipomatosis in the posterior neck and right upper back, in a 18-year-old boy with Proteus syndrome. We report this case of Proteus syndrome and review the literature on this rare disease.

Keyword

anesthetic problems; hamartomatous disorder; proteus syndrome

MeSH Terms

Adolescent
Anesthesia, General
Humans
Incidence
Lipectomy
Lipomatosis
Male
Neck
Proteus Syndrome*
Proteus*
Rare Diseases
Spine