Korean J Pediatr.
2004 Feb;47(2):214-216.
A Case of Systemic Sclerosis in a Child
- Affiliations
-
- 1Department of Pediatrics, College of Medicine, Inha University, Incheon, Korea. sonbk@inha.ac.kr
- 2Department of Internal Medicine, College of Medicine, Inha University, Incheon, Korea.
Abstract
- Systemic sclerosis is a connective tissue disease involving primarily the skin and subcutaneous tissue but may involve other organ systems such as the lungs, gastrointestinal tract, and heart. Systemic sclerosis is a rare childhood disease. The age of onset for patients with systemic sclerosis has its peak between 30 and 50 years of age. Only 1 to 2% of all patients with systemic sclerosis have disease onset before the age of 10 years of age. We report a case of systemic sclerosis in a 7-year-old female who showed Raynaud's phenomenon as an initial manifestation.