Korean J Pediatr.  2005 Feb;48(2):228-231.

A Case of Atypical Teratoid/Rhabdoid Tumor Arising from the Supratentorial Area

Affiliations
  • 1Department of Pediatrics, College of Medicine, Inha University, Incheon, Korea. ysped@inha.ac.kr
  • 2Department of Neurosurgery, College of Medicine, Inha University, Incheon, Korea.
  • 3Department of Pathology, College of Medicine, Inha University, Incheon, Korea.

Abstract

Atypical teratoid/rhabdoid tumor may arise at any central nervous system location, but it is most commonly located in the cerebellum(60 percent). The incidence of this tumor remains unclear but it occurs most commonly in children less than 2 years of age. This highly malignant tumor shows a rapid progression and nonspecific radiologic findings. We report a case of primary intracranial atypical teratoid/rhabdoid tumor arising from the supratentorial area in early infancy. The diagnosis was made based on distinctive light microscopy and immunohistochemical findings. Despite aggressive surgical treatment with adjuvant chemotherapy, he died six months after his second operation.

Keyword

Atypical teratoid/rhabdoid tumor; Supratentorium

MeSH Terms

Central Nervous System
Chemotherapy, Adjuvant
Child
Diagnosis
Humans
Incidence
Microscopy
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