Korean J Otorhinolaryngol-Head Neck Surg.  2016 Jan;59(1):68-72. 10.3342/kjorl-hns.2016.59.1.68.

A Case of Superior Semicircular Canal Dehiscence Syndrome with Coexisting Otosclerosis

• Yang CJ
• Kim SA
• Lee HS
• Park HJ

• KMID: 2277947
• DOI: http://doi.org/10.3342/kjorl-hns.2016.59.1.68

Abstract

Superior semicircular canal dehiscence (SSCD) syndrome and otosclerosis have overlapping clinical manifestations that can be difficult to distinguish. Audiovestibular symptoms are caused by noise or straining in SSCD, which is associated with the presence of an air-bone gap that overlaps with the characteristic of otosclerosis. We recently examined a 51-year-old woman presenting with unilateral pulsatile tinnitus and ipsilateral hearing loss in the left ear. Computerized tomography, audiometry and vestibular function test confirmed the diagnosis of ipsilateral SSCD syndrome with coexisting ipsilateral otosclerosis. The patient underwent surgical repair of dehiscence by middle fossa approach and stapes surgery for otosclerosis sequentially. She has not had pulsatile tinnitus postoperatively, and hearing improved with the closure of air-bone gap at most frequencies. In conclusion, when SSCD syndrome and otosclerosis coexist and patient has representative symptoms of both ear pathologies, a sequential surgery can be an effective treatment option.

Keyword

Otosclerosis; Semicircular canal; Superior semicircular canal dehiscence syndrome

MeSH Terms

Audiometry
Diagnosis
Ear
Female
Hearing
Hearing Loss
Humans
Middle Aged
Noise
Otosclerosis*
Pathology
Semicircular Canals*
Stapes Surgery
Tinnitus
Vestibular Function Tests