Korean J Dermatol.  2006 Aug;44(8):959-961.

A Case of Congenital Onychodysplasia of the Index Fingers Associated with Dandy-Walker Variant

• Shin HJ
• Park J
• Park YL
• Lee JS
• Whang KU

Abstract

Congenital onychodysplasia of the index fingers (COIF) is a rare disorder characterized by various forms of nail dysplasia which are mainly limited to the index fingers. The aetiology of the disease is still a matter of debate. COIF is characterized by five criteria: congenital occurrence, unilateral or bilateral index finger involvement, variability of nail appearance, possible hereditary involvement, and frequently associated bone abnormalities. We report a case of COIF, which is associated with Dandy-Walker variant.

Keyword

Congenital onychodysplasia of the index fingers; Dandy-Walker variant

MeSH Terms

Dandy-Walker Syndrome*
Fingers*