Korean J Dermatol.  2010 Aug;48(8):729-731.

Congenital Onychodysplasia of the Index Fingers with a Y-shaped Bifurcation of the Distal Phalanx

• Kim HJ
• Lee KG
• Yi SM
• Kim JH
• Choi JE
• Son SW
• Kim IH

Abstract

Congenital onychodysplasia of the index fingers (COIF, Iso and Kikuchi syndrome) is a congenital disorder characterized by various forms of nail dysplasias mainly-involving the index fingers. Its etiopathogenesis is still unknown, but ischemia of the palmar digital arteries has been suggested to play a role in this disorder. Although not specific to it, a Y-shaped bifurcation of the distal affected phalanx is a characteristic finding of this syndrome. In this review, we report a case of COIF who presented with bilateral micronychia with a Y-shaped bifurcation of the distal phalanx.

Keyword

Congenital onychodysplasia of the index fingers; Iso and Kikuchi syndrome

MeSH Terms

Arteries
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Fingers
Ischemia
Nails